Giant Cell Arteritis (GCA): Symptoms, Diagnosis and Treatment

Black and white photograph of an older woman holding her temple with subtle red highlight showing temporal artery inflammation in giant cell arteritis

Giant cell arteritis (GCA), also known as temporal arteritis, is a serious inflammatory condition that affects medium and large arteries, particularly those supplying the head, eyes and brain. It is a medical emergency because untreated disease can lead to permanent vision loss, stroke and other life-threatening complications.

Although GCA is highly treatable, early recognition and prompt treatment are critical. Delay in diagnosis can result in irreversible damage within hours or days.

What Is Giant Cell Arteritis?

Giant cell arteritis is a form of large vessel vasculitis, meaning inflammation of blood vessels.

It primarily affects:

  • the temporal arteries

  • arteries supplying the eyes

  • arteries supplying the brain

  • the aorta and its major branches

Inflammation causes:

  • thickening of artery walls

  • narrowing of the vessel lumen

  • reduced blood flow to vital tissues

This reduced blood flow is what leads to visual loss, stroke and tissue damage.

Why Is It Called Giant Cell Arteritis or Temporal Arteritis?

The name giant cell arteritis comes from what pathologists see under the microscope when a sample of an affected artery is examined.

In some patients, the inflamed artery wall contains large immune cells called giant cells. These are formed when multiple inflammatory cells fuse together as part of the immune response.

Not every biopsy shows giant cells, but the name has remained because it reflects a typical microscopic feature of the disease.

What Does “Arteritis” Mean?

The word arteritis simply means inflammation of arteries:

  • artery = a blood vessel that carries blood from the heart

  • -itis = inflammation

So arteritis = inflammation of an artery.

Why Is It Also Called Temporal Arteritis?

The term temporal arteritis is an older name for GCA. It comes from the fact that the temporal arteries — which run along the sides of the head — are often involved and may become tender, thickened or painful.

However, GCA frequently affects other arteries as well, including:

  • arteries supplying the eyes

  • arteries supplying the brain

  • the aorta and its major branches

For this reason, giant cell arteritis is now the preferred and more accurate term.

Who Gets GCA?

GCA almost exclusively affects people over the age of 50, with peak incidence between 70 and 80 years.

  • It is more common in women than men

  • It is more common in people of Northern European ancestry

  • It is one of the most common forms of vasculitis in older adults

The Link Between GCA and Polymyalgia Rheumatica (PMR)

GCA and polymyalgia rheumatica (PMR) are closely related conditions on the same disease spectrum.

  • Around 15–20% of people with PMR will develop GCA

  • Up to 50% of people with GCA have symptoms of PMR

PMR causes:

  • shoulder and hip pain

  • morning stiffness

  • difficulty lifting the arms

  • difficulty getting out of chairs or bed

Because of this close link, anyone with PMR must be monitored carefully for symptoms of GCA.

What Causes GCA?

The exact cause of GCA is not fully understood.

It is believed to involve:

  • immune system dysregulation

  • abnormal activation of inflammatory cells in artery walls

  • excessive cytokine signalling (including interleukin-6)

  • genetic susceptibility

  • possible environmental triggers

This immune-driven inflammation damages the arterial wall and disrupts blood flow.

Common Symptoms of GCA

Symptoms can develop suddenly or over a period of several weeks.

Head and Scalp Symptoms

  • new-onset headache

  • scalp tenderness

  • pain when brushing hair

  • temple pain

  • thickened or tender temporal arteries

Jaw Symptoms

  • jaw pain or fatigue when chewing (jaw claudication)

  • pain that improves with rest

Jaw claudication is highly specific for GCA.

Visual Symptoms

  • blurred vision

  • double vision

  • visual shadows

  • partial vision loss

  • complete sudden blindness

Systemic Symptoms

  • fatigue

  • fever

  • weight loss

  • night sweats

  • loss of appetite

Symptoms of Large-Vessel GCA

When the aorta or its major branches are involved:

  • arm or leg claudication

  • asymmetric blood pressures

  • chest or back pain

  • aortic aneurysm (often silent initially)

Why GCA Is a Medical Emergency

GCA can cause:

  • permanent vision loss

  • stroke

  • aortic aneurysm

  • aortic dissection

Once vision is lost, it is usually irreversible.

For this reason:

Steroid treatment must be started immediately when GCA is suspected — even before the diagnosis is fully confirmed.

(Related reading: Steroids Explained: Benefits, Risks and How They Are Used Safely in Rheumatology)

How Is GCA Diagnosed?

There is no single perfect diagnostic test.

Diagnosis relies on a combination of:

Clinical Assessment

  • age over 50

  • new-onset headache

  • jaw claudication

  • scalp tenderness

  • temporal artery thickening, loss of pulsation

  • visual symptoms

  • symptoms of PMR

Blood Tests

Most patients have raised:

  • ESR

  • CRP

However:

  • inflammatory markers can occasionally be normal

  • normal blood tests do not exclude GCA

(Related reading: Blood Tests in Rheumatology – What Do CRP, ESR and Autoantibodies Really Mean?)

Ophthalmic Assessment

Urgent ophthalmic assessment is essential in anyone with:

  • visual symptoms

  • suspected optic nerve involvement

  • transient visual loss

An ophthalmologist may assess:

  • visual acuity

  • visual fields

  • colour vision

  • optic disc appearance

  • retinal circulation

This helps identify:

  • anterior ischaemic optic neuropathy

  • retinal artery occlusion

Imaging

Doppler Ultrasound

  • vessel wall thickening

  • “halo sign”

PET-CT

  • aortic inflammation and large-vessel involvement

Temporal Artery Biopsy

Shows:

  • arterial wall inflammation

  • sometimes giant cells

Biopsies may be falsely negative.

Treatment should never be delayed.

Treatment of GCA

Immediate Steroid Therapy

  • prednisolone 40–60 mg daily

  • IV steroids for visual symptoms

(Related reading: Steroids Explained)

Steroid Tapering

  • 12–24 months

  • slow reduction

  • relapses common

Steroid-Sparing Treatment: Tocilizumab

Tocilizumab is a biologic medication that blocks interleukin-6.

It:

  • reduces relapse

  • allows faster tapering

  • reduces steroid toxicity

Tocilizumab is usually prescribed through specialist GCA centres such as the Royal Free Hospital.

Monitoring and Long-Term Risks

  • relapse

  • steroid toxicity

  • infection

  • osteoporosis

  • diabetes

  • hypertension

  • aortic aneurysm

(Related reading: DEXA Scans Explained and Osteoporosis Explained)

Why Early Specialist Care Matters

  • urgent diagnosis

  • immediate steroids

  • safe tapering

  • biologic access

  • complication monitoring

In Summary

  • GCA is a medical emergency

  • “arteritis” means inflammation of arteries

  • “giant cells” are inflammatory cells seen on biopsy

  • Immediate steroids prevent blindness

  • Ophthalmic assessment is crucial

  • Imaging and biopsy support diagnosis

  • Tocilizumab reduces steroid exposure

  • Long-term monitoring is essential

Trusted Patient Information Resources

Dr Animesh Singh, Consultant Rheumatologist. GMC: 6130215


Please note, these posts are for general information only and do not constitute medical advice. Dr Singh would encourage you to speak to your healthcare professional to be assessed and managed for your specific symptoms.

If you are concerned that you or a relative has GCA, please seek emergency medical attention through A&E or your GP for assessment.

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